Carnitine O-palmitoyltransférase

Carnitine O-palmitoyltransférase

La carnitine O-palmitoyltransférase (CPT) est une enzyme mitochondriale de type transférase (EC 2.3.1.21), impliquée dans le métabolisme de la palmitoylcarnitine en palmitoyl-CoA.

Une enzyme transférase proche est la carnitine acyltransférase.

Voie métabolique

Acyl-CoA from cytosol to the mitochondrial matrix.gif


CPT chez l'humain

Il existe quatre formes de la CPT chez l'humain:

  • les carnitine palmitoyltransferase I A (CPT1A), B (CPT1B) et C (CPT1B)
  • la carnitine palmitoyltransferase II (CPT2)

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